Search results for "Long survival"

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Survival of patients with spinal muscular atrophy type 1.

2013

BACKGROUND: Spinal muscular atrophy type 1 (SMA1) is a progressive disease and is usually fatal in the first year of life. METHODS: A retrospective chart review was performed of SMA1 patients and their outcomes according to the following choices: letting nature take its course (NT); tracheostomy and invasive mechanical ventilation (TV); continuous noninvasive respiratory muscle aid (NRA), including noninvasive ventilation; and mechanically assisted cough. RESULTS: Of 194 consecutively referred patients enrolled in this study (103 males, 91 females), NT, TV, and NRA were chosen for 121 (62.3%), 42 (21.7%), and 31 (16%) patients, respectively. Survival at ages 24 and 48 months was higher in …

MalePalliative careDatabases Factualmedicine.medical_treatmentKaplan-Meier EstimateSpinal Muscular Atrophies of ChildhoodSeverity of Illness IndexCohort StudiesRetrospective StudieCause of DeathPalliative CarePrognosisSpinal muscular atrophy type 1Child PreschoolHome mechanical ventilationBreathingFemaleLong survivalSurvival AnalysiPediatric palliative careHumanmedicine.medical_specialtyPrognosiMechanical assisted coughRisk AssessmentStatistics NonparametricArts and Humanities (miscellaneous)medicineRespiratory muscleConfidence IntervalsHumansDecompensationSurvival analysisRetrospective StudiesMechanical ventilationNoninvasive Ventilationbusiness.industryInfant NewbornOxygen Inhalation TherapyInfantSpinal muscular atrophymedicine.diseaseRespiration ArtificialSurvival AnalysisConfidence intervalSurgeryPediatrics Perinatology and Child HealthCohort StudiebusinessConfidence IntervalPediatrics
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